Figure 2. Immunohistochemical analysis of proband's biceps muscle. (A) Modified Gomori trichrome stain (40X). (B) Reduced nicotinamide adenine dinucleotide-tetrazolium reductase (NADH-TR) stain (40X). (C) Combined succinic dehydrogenase and cytochrome oxidase (SDH/COX) stain (40X). Ragged red and blue fibers are seen in panels A and B, respectively.  COX-negative fibers are evident in panel C, where fibers devoid of COX activity (C) appear blue.
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